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TYPE III CPAM- A CASE REPORT OF A RARE VARIANT
EP33144
Poster Title: TYPE III CPAM- A CASE REPORT OF A RARE VARIANT
Submitted on 14 Oct 2020
Author(s): DR.PREETHI PHILOMINA, Co-Authors :DR.ANINDITA MISHRA(HOD), DR.L.SRIKANTH. GSL MEDICAL COLLEGE, INDIA
Affiliations: GSL MEDICAL COLLEGE AND GENERAL HOSPITAL ,INDIA
This poster was presented at BIR(BRITISH INSTITUTE OF RADIOLOGY) ANNUAL CONGRESS 2020
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Poster Information
Abstract: CPAM (Congenital Pulmonary Airway Malformation ) formerly called CCAM (Congenital Cystic Airway Malformation) is a rare fetal thorax congenital anomaly , which is a hamartomatous malformation of lung characterized by abnormal branching of immature bronchioles. With the evolution of high resolution ultrasound, it is detected in early antenatal scans.(1)
CPAM is mainly of 3 types. TYPE III is the rarest with the incidence of about 5% of all cases and is associated with the poorest prognosis of all(2) . Unlike type I & II, this also has a different appearance on ultrasound, being solid and not cystic.
Hence this case report highlights the importance of detecting and diagnosing such an entity for proper early decision and management. Role of sonography in evaluation of prognostic factors and outcome apart from diagnosis, is also discussed .(1)
Summary: Type I & II are cystic in appearance but type III appears solid on sonography due to multiple reflecting echoes.
Type III ,the rarest form of CPAM thus stands as a potential DD for an HYPERECHOIC MASS in fetal thorax.
Type III has highest risk of pulmonary hypoplasia, tendency of growth, mass effect(solid), early development of hydrops and polyhydramnios.
Detection of hyperechoic mass with above features favoring CPAM TYPE III leads to early and efficient decision.
References: (1)CALLEN’S ULTRASONOGRAPHY IN OBSTETRICS AND GYNECOLOGY
(2)Sirithangkul S, Chuengchitraks S, Staworn D, Laohapand C, Silarat T. Late manifestation of congenital cystic adenomatoid malformation with lung abscess: a case report. J Med Assoc Thai. 2010;93 Suppl 6:S223-S227.
(3)Azizkhan RG, Crombleholme TM. Congenitalcystic lung disease: contemporary antenatal and postnatal management. Pediatr Surg Int 2008;24(6):643–657
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